Hosting 723 files, 2931 images, and 4 contributors.

Random Case

Transient Tachypnea of the Newborn
Joseph Junewick, MD FACR
over 6 years ago
Enter A Workflow
Standard2   Academic2

Please choose a workflow. A standard workflow allows you to browse the repository with full case detail; the academic workflow allows you to browse the repository with limited case detail revealed. Double click on the images to launch image viewer.

ARSt Case Repository

Case History

Teenager with tachycardia

Case Detail

Anatomy: Chest
Joseph Junewick, MD FACR
Diagnostic Category: Genetic or Congenital
Created: over 9 years ago
Updated: over 9 years ago
Tags: PEDS
Modality/Study Types: MR
Adobe32 PDF Imagej32 ImageJA

Case Images

Academic Case Revealer (Click to Expand)

Reveal Findings

MRI reveals decreased right ventricular free wall thickness and T1 hyperintensity of the infundibulum. Poor right ventricular contractility was noted on cinegraphic imaging.

Reveal Discussion

ARHS presents in young and middle age patients with ventricular dysrhythmia and left bundle branch block and occasionally sudden death. Males are three times more often affected than females and there is usually a strong family history. MR is the preferred imaging modality to confirm the diagnosis. T1 hyperintensity in the right ventricular outlet tract corresponds to fat and is associated with a higher incidence of inducible tachycardia. Cinegraphic imaging helps determine right ventricular function and wall motion abnormalities. Treatment includes anti-arrhythmic drugs, ablation, defibrillator and/or ventriculotomy. The risk of death is 1% per year.

Reveal Diagnosis

Arrythmogenic Right Heart Syndrome (ARHS)

Corporate Office: 616.363.7272, 3264 North Evergreen Drive, Grand Rapids, MI 49525

Spectrum Health Helen Devos Childrens Hospital GE HealthCare