Hosting 721 files, 2924 images, and 4 contributors.

Random Case

Multiple Thyroid Colloid Cysts
Joseph Junewick, MD FACR
over 8 years ago
Enter A Workflow
Standard2   Academic2

Please choose a workflow. A standard workflow allows you to browse the repository with full case detail; the academic workflow allows you to browse the repository with limited case detail revealed. Double click on the images to launch image viewer.

ARSt Case Repository

Congenital Cholesteatoma

Case Detail

Anatomy: Neck-Face
Joseph Junewick, MD FACR
Diagnostic Category: Developmental or Congenital
Created: over 4 years ago
Updated: about 1 year ago
Tags: PEDS
Modality/Study Types: CT
Adobe32 PDF Imagej32 ImageJA


3 year old male with pearl white tympanic membrane noted on well-child examination.

Case Images


Congenital Cholesteatoma


CT – Noncontrast axial and coronal images of the left temporal bone show a small rounded soft tissue mass medial to the ossicular chain (contiguous with the cochlear promontory and malleus) but not associated with ossicular erosion.


Congenital cholesteatomas are usually clinically asymptomatic and may occur anywhere in the temporal bone – middle ear cavity, mastoid air cells, petrous apex and the squama. Macroscopically, cholesteatomas are pearly gray or yellow circumscribed lesions. The pathophysiology is thought to be related to persistent fetal epithelium, epidermoid cyst equivalent. Ossicular erosion is unusual with congenital cholesteatomas or occurs late in the course. Congenital cholesteatomas can be associated with external auditory atresia and branchial cleft remnants.


Barth K, Huber AM, Stampfli P, et al. Neuroradiology of cholesteatomas. AJNR (2011); 32:221-229.

Corporate Office: 616.363.7272, 3264 North Evergreen Drive, Grand Rapids, MI 49525

Spectrum Health Helen Devos Childrens Hospital GE HealthCare