Hosting 718 files, 2916 images, and 4 contributors.

 
Random Case

Isolated Uterine Tube Torsion
Joseph Junewick, MD FACR
over 6 years ago
Enter A Workflow
Standard2   Academic2

Please choose a workflow. A standard workflow allows you to browse the repository with full case detail; the academic workflow allows you to browse the repository with limited case detail revealed. Double click on the images to launch image viewer.

ARSt Case Repository

Chiari I with Syringomyelia

Case Detail

Anatomy: Brain-Spine
Junewick
Joseph Junewick, MD FACR
Diagnostic Category: Developmental or Congenital
Created: over 5 years ago
Updated: over 5 years ago
Tags: PEDS
Modality/Study Types: MR
Activities:
Adobe32 PDF Imagej32 ImageJA

History

Teenager with headache and upper extremity weakness.


Case Images


Diagnosis

Chiari I with Syringomyelia

Findings

MR – Sagittal T1 and T2 images show pegged tonsils and large beaded central syrninx.

Discussion

Chiari I malformation is a congenital hindbrain dysgenesis characterized by downward displacement of cerebellar tonsils through the foramen magnum into the spinal canal. The exact criteria by which tonsillar ectopia should be considered abnormal has been a controversial issue but in general requires tonsillar herniation of at least 5mm. Patients with Chiari I malformations may remain asymptomatic often present with symptoms relating to hindbrain compression, such as headache, weakness, numbness, ataxia. When syringomyelia is present (seen in 30% – 56% in Chiari I patients), additional findings could include central cord syndrome, impaired sensation, scoliosis, spasticity, and torticollis. MRI is the imaging modality of choice to diagnose Chiari I malformation and associated impaired CSF flow and syringomyelia.

Reference

Elster AD, Chen MY. Chiari I Malformations: Clinical and Radiologic Reappraisal. Radiology (1992); 183:347-353.

Contributor

Rekha Meesa, MD



Corporate Office: 616.363.7272, 3264 North Evergreen Drive, Grand Rapids, MI 49525

Spectrum Health Helen Devos Childrens Hospital GE HealthCare