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Joseph Junewick, MD FACR
over 6 years ago
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Cervical Syrinx with Chiari I

Case Detail

Anatomy: Brain-Spine
Junewick
Joseph Junewick, MD FACR
Diagnostic Category: Developmental or Congenital
Created: over 5 years ago
Updated: over 5 years ago
Tags: PEDS
Modality/Study Types: MR
Activities:
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History

5 year old male with headache.


Case Images


Diagnosis

Cervical Syrinx with Chiari I

Findings

MR – Sagittal T1 and T2 images show “pegged” cerebellar tonsils extending to the level of C2 with fusiform syrinx at the cervicothoracic junction.

Discussion

Chiari I malformation is defined by downward displacement of the cerebellar tonsils of 5 mm or more. Although Chiari I malformation is not usually associated with other intracranial abnormalities, syringomyelia is found in 20–70% of patients, depending on the degree and extent of disruption of normal cerebrospinal fluid flow between the spine and cranium. Syrinx associated with Chiari I malformation is more common in older children, girls and those with greater degree of CSF obstruction. Surgical decompression at the craniocervical junction often resovles the syrinx and associated neuronal dysfunction although occasionally syrinx shunting is required.

Reference

Strahle J, Muraszko KM, Kapurch J, et al. Chiari malformation Type I and syrinx in children undergoing magnetic resonance imaging. J Neurosurg Pediatr (2011); 8(2):205-13.



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