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Orbital Hemangioma
Joseph Junewick, MD FACR
over 6 years ago
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Dermatomyositis - Truncal

Case Detail

Anatomy: Musculoskeletal
Junewick
Joseph Junewick, MD FACR
Diagnostic Category: Infectious-Inflammatory
Created: over 6 years ago
Updated: over 5 years ago
Tags: PEDS
Modality/Study Types: CT
Activities:
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History

Teenager with abdominal pain.


Case Images


Diagnosis

Dermatomyositis

Findings

CT – Multiplanar images show extensive truncal subcutaneous and fascial calcifications.

Discussion

Dermatomyositis is a rare immune-related myopathic disorder. Clinical presentation includes subacute to acute onset of proximal muscle weakness and a range of erythematous skin changes. The classic dermatologic manifestations include a heliotrope rash of the upper eyelids and bluish red plaques on the backs of the knuckles. Increased serum creatine kinase, dysphagia, and interstitial lung disease may also be seen. Pathogenesis of dermatomyositis is characterized by immune complex deposition in vessel walls and the presence of microtubuloreticular structures in endothelial cells. Definitive diagnosis of dermatomyositis requires a muscle biopsy to distinguish it from other immune-related myopathic disorders. The risk for cancer is increased in these patients.

Reference

Postolov I, Rasiej MJ, Hershman D, et al. Thoracoabdominal Muscular Enlargement in Dermatomyositis: CT Visualization
AJR (2005); 184:S91-S93.



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