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Bilateral Choanal Atresia
Joseph Junewick, MD FACR
over 4 years ago
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Chondromesenchymal hamartoma

Case Detail

Anatomy: Neck-Face
Junewick
Joseph Junewick, MD FACR
Diagnostic Category: Genetic or Congenital
Created: over 8 years ago
Updated: over 7 years ago
Tags: PEDS
Modality/Study Types: MR CT
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History

Infant with biphasic stridor and retractions requiring tracheostomy at birth.


Case Images


Diagnosis

Chondromesenchymal hamartoma

Clinical Notes

Paralyzed right vocal cord at laryngoscopy.

Findings

CT – Soft tissue mass in right nasal cavity with few punctate internal calcifications associated with destruction of the the posterior nasal septum and medial right orbital wall.

MRI – Non-enhancing right laryngeal mass which is isointense to cartilage on all sequences.

Discussion

Nasal hamartomas are either of epithelial (e.g., respiratory epithelium, salivary gland epithelium, or seromucinous epithelium) or mesenchymal origin (e.g., chondroid, lipomatous, or angiomatous); both are named by their predominant component.

Chondromesenchymal hamartomas (CH) are rare. CH usually present during infancy with nasal obstruction although may be occasionally seen in teenagers or adults. CH are likely congenital but genetic, endocrine and environmental factors may influence. While lesions can be locally destructive, surgical excision is curative.

Reference

Johnson C, et al. Nasal chondromesenchymal hamartoma: radiographic and histopathologic analysis of a rare pediatric tumor. Ped Radiol 2008; 37(1):101-104.



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