Hosting 718 files, 2916 images, and 4 contributors.

 
Random Case

UVC Related Hepatic Injury
Joseph Junewick, MD FACR
over 8 years ago
Enter A Workflow
Standard2   Academic2

Please choose a workflow. A standard workflow allows you to browse the repository with full case detail; the academic workflow allows you to browse the repository with limited case detail revealed. Double click on the images to launch image viewer.

ARSt Case Repository

Melanotic neuroectodermal tumor of infancy

Case Detail

Anatomy: Genitourinary
Junewick
Joseph Junewick, MD FACR
Diagnostic Category: Neoplasia Benign
Created: over 8 years ago
Updated: over 8 years ago
Tags: PEDS
Modality/Study Types: US
Activities:
Adobe32 PDF Imagej32 ImageJA

History

Nearly 5 month old male with scrotal mass.


Case Images


Diagnosis

Epididymal melanotic neuroectodermal tumor of infancy

Clinical Notes

Elevated vanillylmandelic acid (VMA).

Findings

US – Hydrocele with hypervascular mass adjacent to the normal testicle.

Gross Pathology – The tumor originates from the epididymus. The cut surface of the tumor is white and fibrous with a punctate central dark spot.

Discussion

Melanotic neuroectodermal tumor of infancy (MNTI) is a rare tumor. More than 90% involve the head and heck (most often the maxilla) but skin, mediastinum, long bones, uterus, ovary and epididymus have been reported. MNTI are almost always solitary with an average age of onset between 1 and 6 months. While MNTI grow very rapidly, the clinical course is benign with only 15% incidence of local recurrence.

Reference

Lee SB et al. Melanotic Neuroectodermal Tumor of Infancy in the Epididymus: A Case Report. Kor J Ped (2004); 47(12):1334-7.



Corporate Office: 616.363.7272, 3264 North Evergreen Drive, Grand Rapids, MI 49525

Spectrum Health Helen Devos Childrens Hospital GE HealthCare