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Renal Cortical Necrosis
Joseph Junewick, MD FACR
over 6 years ago
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Chordoma

Case Detail

Anatomy: Brain
Junewick
Joseph Junewick, MD FACR
Diagnostic Category: Neoplasia Malignant
Created: over 8 years ago
Updated: over 7 years ago
Tags: PEDS
Modality/Study Types: MR CT
Activities:
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History

15 year old male with difficulty speaking and slowly progressive ataxia.


Case Images


Diagnosis

Chordoma (myxoid variant)

Findings

CT – well circumscribed low density extra-axial mass containing a single punctate calcification.

MRI – T1 hypointense, T2 hyperintense mass; scattered punctate intralesional enhancement with whispy enhancement emanating from the basisphenoid synchondrosis are present. No osseous destruction or infiltration is demonstrated.

MRS – Absent NAA and choline peaks and elevated lipid and lactate peaks.

Discussion

Chordomas originate from notochordal remnants and consequently have fairly predictable locations, cranial (32%), spinal (32%), sacral (29%) and other sites. Chordomas can occur at any age but are most commonly seen in the fourth decade of life. Males are twice as likely as females to be affected. They are slow growing tumors with insidious symptoms; intracranial tumors most often present with headache and cranial neuropathy. Most cases are associated extensive osseous destruction.



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