Circumflex Retroesophageal Right Aortic Arch
Joseph Junewick, MD FACR
over 5 years ago
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Heather Borders, MD
|Diagnostic Category: Developmental or Congenital
|Created: over 7 years ago
|Updated: over 7 years ago
Three year old patient with seizures.
A thick band of gray matter (parallels the intensity of gray matter on all sequences) separated from the outer cortex and ventricles by layers of white matter. The outer cortex shows subjective mildly shallow sulci.
Band Heterotopia typically presents in childhood due to developmental delay and mixed seizures. There is a female preponderance due to the location of DCX on the X chromosome.
On imaging, there is a homogeneous band of gray matter located between the ventricles and the cerebral cortex and separated from both by layers of white matter. Overlying cortex is usually normal in thickness and there is variablility in the degree of shallowness of the sulci.
This may be mistaken for myelinating white matter in a neonate unless the cell sparse zone is visible.